FRCA Notes


Post-Hypoxic Myoclonus

This topic almost certainly lies outside the purview of the FRCA exams, though is included here for personal reference after being asked by a junior colleague how to manage such seizures in a post-resuscitation patient during the middle of the night.

Resources


  • Seizures are a common (20 - 30%) phenomenon in the post-resuscitation patient on ICU
  • They can be diagnosed via:
    • Clinically observed convulsions
    • Typical EEG seizure activity (electrographic seizure)
  • There is often substantial overlap, with both clinical and EEG seizures present
  • Clinical seizures, however, may only become apparent during sedation holds owing to the seizure-suppressive effects of propofol/benzodiazepines
  • Although EEG is beneficial, continuous EEG monitoring probably adds little except cost and tangled wires

Myoclonic seizures

  • The most common seizure type in post-arrest patients (approx. 2/3rds)
  • May be focal, multi-focal or generalised
  • Origin is predominantly cortical, but may arise subcortically
  • Develops in the first 48hrs post-arrest
  • May be transient i.e. cease by 1 week post-arrest
  • Often associated with a poor prognosis
    • Post-hypoxic myoclonic status epilepticus is associated with a >95% mortality or PVS rate (<2% survive with good neurological outcome)
    • Conversely, single seizure events or sporadic focal myoclonus do not predict poor outcome

Lance-Adams syndrome

  • A type of myoclonic seizure in the post-resuscitation patient who regains consciousness
  • More common after hypoxic cardiac arrest
  • Develops days or weeks post-arrest
  • Predominantly affects the limbs
  • Myoclonus is induced by purposeful motor movement or sensory stimulation
  • May be chronic and disabling
  • Cannot be distinguished from 'standard' myoclonus on EEG

Other

  • Focal seizures
  • Generalised tonic-clonic seizures

Prophylaxis

  • Both Resus Council (2021) and ERC/ESICM (2021) guidelines do not advise seizure prophylaxis, acknowledging that the evidence base is very low certainty

Treatment of seizures

  • Conversely, both the aforementioned guidelines suggest treating seizures if they arise, again acknowledging that the evidence base is very low certainty
  • The increased CMRO2 caused by seizure activity may exacerbate cerebral injury and therefore treatment is reasonable
  • Treatment of post-hypoxic myoclonic status epilepticus is difficult

  • Does treating seizures affect outcome?
    • The recent TELSTAR trial (NEJM, 2022) randomised post-resuscitation patients to a protocolised 48hr anti-seizure regimen vs. standard care alone
    • There was no difference in 90-day neurological outcome or 90-day mortality between the arms
    • Those in the intervention arm had slightly longer durations of mechanical ventilation and ICU stay

    • A case series demonstrated up to 44% of patients with post-anoxic status epilepticus had a good outcome following treatment with multiple anti-epileptic drugs; of note those treated had delayed awakening too

Choice of drug(s)

  • There is limited evidence that conventional anti-epileptic drugs suppress EEG epileptiform activity in the post-resuscitation patient, despite suppressing myoclonus of other origin
  • If conventional anti-epileptics are to be used, choices include:
    • (Fos)phenytoin
      • Phenytoin can cause hypotension via negative inotropic and vasodilating effects, especially if rapidly administered, so is less suitable
      • Fosphenytoin equally caused more hypotension compared to other agents when used to treat status epilepticus
    • Levetiracetam
    • Valproate
  • Each is equally effective in terminating 'traditional' convulsive status epilepticus (NEJM, 2019)
  • Be mindful that treatment can delay awakening, prolong duration of mechanical ventilation and ICU stay

  • Another option is use of general anaesthetic agents, which the patient is probably already receiving via infusion, e.g. propofol, a benzodiazepine or thiopentone
  • One perhaps has to be mindful that excessive drug administration may cloud brainstem death testing from 72hrs

Treatment regimen

  • The TELSTAR protocol was three tiered:

Tier Sedative Agent Anti-epileptic Agent
1 Midazolam or lorazepam infusion Phenytoin 15 - 20mg/kg loading then 150mg BD
2 Propofol up to 8mg/kg/hr Keppra (1.5g loading then 1g BD) or valproate
3 Thiopentone

  • As one's patient on a UK ICU is likely to already be receiving a propofol infusion, it seems sensible to:
    1. Up-titrate the propofol infusion, until either clinician discomfort or haemodynamics preclude further increases (say 30 - 35ml/hr of 1% propofol)
    2. Add in further agent(s) if seizures persist and are causing harm e.g. difficulty ventilating appropriately, lines being displaced etc.
      • E.g. addition of a midazolam infusion ± keppra loading
    3. Strongly consider whether further pharmacotherapy will add patient benefit if seizures continue despite the above